FAMILIAL MEDITERRANEAN FEVER: A STUDY OF 32 CASES
نویسندگان
چکیده مقاله:
From April 1983 to September 1990, 32 patients with familial mediterranean fever (FMF) were studied. FMF is characterized by short, self-limited, febrile episodes that occur with inflammation of serosal surfaces. Major symptoms include fever and abdominal pain, presenting as acute surgical abdomen. These attacks are associated with considerable morbidity and in some patients lead to unnecessary surgery. Diagnosis of this disease depends on the absence of any objective markers and the recognition of the symptoms in a susceptible individual. Duration of disease on admission was 1.5-19 years. Except in two pairs of siblings, no familial association was noted. This is the first review of the cases of FMF from Iran.
منابع مشابه
familial mediterranean fever: a study of 32 cases
from april 1983 to september 1990, 32 patients with familial mediterranean fever (fmf) were studied. fmf is characterized by short, self-limited, febrile episodes that occur with inflammation of serosal surfaces. major symptoms include fever and abdominal pain, presenting as acute surgical abdomen. these attacks are associated with considerable morbidity and in some patients lead to unnecessary...
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متن کامل[Familial Mediterranean fever].
Familial Mediterranean fever (FMF) is an inherited multisystem disease manifested by painful, febrile attacks affecting the chest, abdomen, joints, and skin. No simple studies confirm the presence of FMF, contributing to the difficulty in diagnosis. A 10-year-old boy initially presented with a diffuse rash and complaints of bilateral joint pain of the hips, knees, and ankles and pain of the rig...
متن کاملFamilial Mediterranean fever.
BACKGROUND The pathogenesis of familial Mediterranean fever (FMF) is unknown, and since no specific laboratory test is yet available, the diagnosis of FMF remains clinical. The purpose of this study was to review clinical characteristics of patients with FMF. METHODS A total of 96 patients with FMF were evaluated either retrospectively (for those diagnosed before 1997) or prospectively (for t...
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عنوان ژورنال
دوره 5 شماره 3
صفحات 97- 100
تاریخ انتشار 1991-11
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